Pulmonary fibrosis

How CenterWell Specialty Pharmacy® can help

Pulmonary fibrosis (PF) is a chronic lung disease that makes it difficult to breathe. Living with PF can be challenging, but it’s possible to manage symptoms and live a full, meaningful life. Learn more about the condition and what we can do to support you on the road ahead.

What is pulmonary fibrosis?¹

PF is a progressive disorder that causes scarring and thickening of the lung tissue. This scarring makes it difficult for oxygen to pass through the lungs, leading to shortness of breath, fatigue and other symptoms.

In people with PF, the lungs have a hard time working properly, causing low oxygen levels in the bloodstream. Ultimately, PF progresses over time, resulting in potentially life-threatening respiratory complications.

The exact cause of PF is unknown, but it’s thought to be a combination of factors, including certain autoimmune diseases (such as rheumatoid arthritis or lupus) and exposure to toxins that can irritate the lungs.

Certain risk factors for PF include:

  • Age: more likely to affect middle-aged and older adults
  • Cancer treatments: radiation treatment or certain chemotherapy drugs
  • Certain occupations: work in mining, farming, or construction due to exposure to certain toxins
  • Genetic factors: some individuals might be more prone to developing PF
  • Sex: men are at risk slightly more than women
  • Smoking: long-term exposure to inhaled smoke  

PF is a serious disease, but it can be managed with proper treatment and medications. There are also several resources to help PF patients cope with the physical and emotional challenges of living with the progressive disease.


PF symptoms may be mild at first, but they tend to progress over time. The rate of the disease’s progression varies from patient to patient. It’s important to meet with your doctor to test for PF if you’re experiencing common symptoms, such as:²

  • Aches in the joints or muscles
  • Chest discomfort
  • Dry cough
  • Fatigue and tiredness
  • Shortness of breath
  • Unintended weight loss
  • Widening and rounding of the tops of the fingers or toes (also referred to as clubbing)

There is no cure for PF, and the lung damage caused by the disease can’t be reversed. Still, treatments like supplemental oxygen use or cough suppressants can help to manage symptoms. There are also medications available to help slow the disease’s progression.

CenterWell Specialty Pharmacy offers medications to treat PF, as directed by your prescriber.

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Getting involved with your community

Whether it’s learning more about the condition, joining a support group or contributing to message boards, you can make a difference for others living with PF.

Specialists who work remotely to support you wherever you are

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Emotional support

Get 1-on-1 support from healthcare professionals who understand what you’re going through. We’ll listen to your concerns, answer your questions and help you manage any stress or anxiety.

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Financial assistance

Don’t stress the bills. We work with financial assistance programs like grants, foundations and manufacturers to help you get the care you need. We’ll also assist you with the application process.

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Clinical guidance

Receive personalized support regularly and instructions on how to take your meds. We’ll also work with your doctor to adjust your therapy if you’re experiencing side effects.

Sources

  1. Pulmonary Fibrosis Information Guide,” Pulmonary Fibrosis Foundation, last accessed Feb. 1, 2024.
  2. Symptoms of Pulmonary Fibrosis,” American Lung Association, last accessed Feb. 1, 2024.